NCCN Guidelines

Soft Tissue Sarcoma

Guidelines

- Alveolar Rhabdomyosarcoma

- Alveolar Soft Part Sarcoma

- Angiomatoid fibrous histiocytoma

- Angiosarcoma

- Atypical Lipomatous Tumor and Well-Differentiated Liposarcoma

- Carney-Stratakis syndrome (gastric GIST and paraganglioma)

- Clear cell sarcoma

- Congenital/infantile-fibrosarcoma

- Dedifferentiated Chordoma

- Dedifferentiated liposarcoma

- Dermatofibrosarcoma Protuberans

- Dermatofibrosarcoma Protuberans (DFSP) with Fibrosarcomatous Transformation

- Desmoid fibromatosis

- Desmoid Tumors (Aggressive Fibromatosis)

- Desmoplastic Small Round Cell Tumor

- Embryonal rhabdomyosarcoma

- Epithelioid hemangioendothelioma

- Epithelioid sarcoma

- Ewing Sarcoma/peripheral neuroectodermal tumor

- Extrarenal rhabdoid tumor

- Extraskeletal myxoid chondrosarcoma

- Extraskeletal Osteosarcoma

- Extremity/Body Wall, Head/Neck

- Gastrointestinal Stromal Tumors (GIST)

- High-grade endometrial stromal sarcomas

- Inflammatory myofibroblastic tumor

- Inflammatory Myofibroblastic Tumor (IMT) with ALK Translocation

- Leiomyosarcoma

- Low grade fibromyxoid sarcoma

- Malignant peripheral nerve sheath tumor

- Malignant Perivascular Epithelioid Cell Tumor (PEComa)

- Mesenchymal chondrosarcoma

- Myxoid/round cell liposarcoma

- NTRK-rearranged spindle cell neoplasm

- Pigmented Villonodular Synovitis/Tenosynovial Giant Cell Tumor

- Pleiomorphic liposarcoma

- Recurrent Angiomyolipoma/Lymphangioleiomyomatosis

- Retroperitoneal Well-Differentiated or Dedifferentiated Liposarcoma

- Retroperitoneal/Intra-Abdominal

- Rhabdomyosarcoma

- Soft Tissue Sarcoma

- Soft Tissue Sarcoma of the Extremity/Superficial Trunk, Head/Neck

- Solitary Fibrous Tumor

- Synovial sarcoma

- Undifferentiated Pleomorphic Sarcoma

- Undifferentiated round cell sarcoma

Evidence Blocks

Guidelines for Patients

International

Harmonized